Primary Ewing Sarcoma of Sphenoid Bone with Intracranial Extension:
A Common Tumour at an
Uncommon Location
Published: February 1, 2017 | DOI: https://doi.org/10.7860/JCDR/2017/23541.9275
Guddi Rani Singh, Vijayanand Choudhary, Rawi Agrawal
1. Senior Resident, Department of Pathology, Indira Gandhi Institute of Medical Sciences, Patna, Bihar, India.
2. Additional Professor, Department of Pathology, Indira Gandhi Institute of Medical Sciences, Patna, Bihar, India.
3. Senior Resident, Department of Pathology, Indira Gandhi Institute of Medical Sciences, Patna, Bihar, India.
Correspondence
Rawi Agrawal,
305, Ushakunj Apartment, Ambedkar Path, Jagdeopath, Bailey Road-800014, Patna, Bihar, India.
E-mail: agrawalrawi@gmail.com
Primary Ewing Sarcoma of the cranial bone is rare, contributing to only 1% of all Ewing Sarcomas. Primary cranial Ewing Sarcoma occurs most commonly in temporal bone followed by parietal and occipital bones. Sphenoid bone is less commonly involved. We report a case of Ewing Sarcoma of the sphenoid bone with intra-cranial extension in a 20-month-old boy. On CT scan a provisional diagnosis of rhabdomyosarcoma was made. Fine Needle Aspiration Cytology (FNAC) and histopathological examination of core needle biopsy showed small round cell tumour. On Immunohistochemistry (IHC), CD99 (MIC2) and FLI 1 were strongly positive and final diagnosis of Ewing Sarcoma was made. Considering the rarity of this unusual site, we report a case of primary Ewing Sarcoma arising in the sphenoid bone with erosion of adjacent bones and intra-cranial extension.
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